<?xml version="1.0" encoding="UTF-8"?>
<!DOCTYPE article PUBLIC "-//NLM//DTD JATS (Z39.96) Journal Publishing DTD v1.3 20210610//EN" "JATS-journalpublishing1-3.dtd">
<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">vestar</journal-id><journal-title-group><journal-title xml:lang="ru">Вестник аритмологии</journal-title><trans-title-group xml:lang="en"><trans-title>Journal of Arrhythmology</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">1561-8641</issn><issn pub-type="epub">2658-7327</issn><publisher><publisher-name>НАО «Инкарт»</publisher-name></publisher></journal-meta><article-meta><article-id custom-type="elpub" pub-id-type="custom">vestar-587</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>ОРИГИНАЛЬНЫЕ ИССЛЕДОВАНИЯ</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>ORIGINAL ARTICLES</subject></subj-group></article-categories><title-group><article-title>АРИТМОГЕННАЯ КАРДИОМИОПАТИЯ/ДИСПЛАЗИЯ ПРАВОГО ЖЕЛУДОЧКА КАК ПРИЧИНА ВНЕЗАПНОЙ СЕРДЕЧНОЙ СМЕРТИ МОЛОДЫХ ЛЮДЕЙ</article-title><trans-title-group xml:lang="en"><trans-title>ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY/DYSPLASIA AS A CAUSE OF SUDDEN CARDIAC DEATH OF YOUNG ADULTS</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Гордеева</surname><given-names>М. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Gordeeva</surname><given-names>M. V.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Митрофанова</surname><given-names>Л. Б.</given-names></name><name name-style="western" xml:lang="en"><surname>Mitrofanova</surname><given-names>L. B.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Пахомов</surname><given-names>А. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Pakhomov</surname><given-names>A. V.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Велеславова</surname><given-names>О. Е.</given-names></name><name name-style="western" xml:lang="en"><surname>Veleslavova</surname><given-names>O. E.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Берман</surname><given-names>М. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Berman</surname><given-names>M. V.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-3"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Иевлева</surname><given-names>Е. Л.</given-names></name><name name-style="western" xml:lang="en"><surname>Ievleva</surname><given-names>E. L.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-3"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Лаврентюк</surname><given-names>Г. П.</given-names></name><name name-style="western" xml:lang="en"><surname>Lavrentyuk</surname><given-names>G. P.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-4"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Платонов</surname><given-names>П. Г.</given-names></name><name name-style="western" xml:lang="en"><surname>Platonov</surname><given-names>P. G.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-4"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Шубик</surname><given-names>Ю. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Shubik</surname><given-names>Yu. V.</given-names></name></name-alternatives><email xlink:type="simple">noemail@neicon.ru</email><xref ref-type="aff" rid="aff-1"/></contrib></contrib-group><aff xml:lang="ru" id="aff-1"><institution>Научно-клинический и образовательный центр «Кардиология» СПбГУ, Россия</institution><country>Russian Federation</country></aff><aff xml:lang="ru" id="aff-2"><institution>ФЦСКиЭ им. В.А.Алмазова, Россия</institution><country>Russian Federation</country></aff><aff xml:lang="ru" id="aff-3"><institution>Северо-западный ГМУ им. И.И.Мечникова</institution><country>Russian Federation</country></aff><aff xml:lang="ru" id="aff-4"><institution>Лундский университет, Швеция</institution><country>Russian Federation</country></aff><pub-date pub-type="collection"><year>2012</year></pub-date><pub-date pub-type="epub"><day>22</day><month>09</month><year>2020</year></pub-date><volume>69</volume><issue>69</issue><fpage>38</fpage><lpage>48</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Гордеева М.В., Митрофанова Л.Б., Пахомов А.В., Велеславова О.Е., Берман М.В., Иевлева Е.Л., Лаврентюк Г.П., Платонов П.Г., Шубик Ю.В., 2020</copyright-statement><copyright-year>2020</copyright-year><copyright-holder xml:lang="ru">Гордеева М.В., Митрофанова Л.Б., Пахомов А.В., Велеславова О.Е., Берман М.В., Иевлева Е.Л., Лаврентюк Г.П., Платонов П.Г., Шубик Ю.В.</copyright-holder><copyright-holder xml:lang="en">Gordeeva M.V., Mitrofanova L.B., Pakhomov A.V., Veleslavova O.E., Berman M.V., Ievleva E.L., Lavrentyuk G.P., Platonov P.G., Shubik Y.V.</copyright-holder><license xml:lang="ru" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>Данная работа распространяется под лицензией Creative Commons Attribution 4.0.</license-p></license><license xml:lang="en" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://vestar.elpub.ru/jour/article/view/587">https://vestar.elpub.ru/jour/article/view/587</self-uri><abstract><p>С целью исследования особенностей заболевания анализируются 18 случаев внезапной сердечной смерти молодых людей в возрасте 14-35 лет с документированной аритмогенной кардиомиопатией/дисплазией правого желудочка.</p></abstract><trans-abstract xml:lang="en"><p>To study peculiar features of the disease, the cases of 18 sudden cardiac deaths in young adults aged 14-35 years with the documented right ventricular arrhythmogenic cardiomyopathy/dysplasia were analyzed.</p></trans-abstract><kwd-group xml:lang="ru"><kwd>аритмогенная кардиомиопатия/дисплазия правого желудочка</kwd><kwd>внезапная сердечная смерть</kwd><kwd>алкоголь</kwd><kwd>наркотики</kwd><kwd>дисплазия соединительной ткани</kwd><kwd>миокардит</kwd><kwd>желудочковые аритмии</kwd><kwd>магнитно-резонансная томография</kwd></kwd-group><kwd-group xml:lang="en"><kwd>right ventricular arrhythmogenic cardiomyopathy/dysplasia</kwd><kwd>sudden cardiac death</kwd><kwd>alcohol</kwd><kwd>illicit drugs</kwd><kwd>connective tissue dysplasia</kwd><kwd>myocarditis</kwd><kwd>ventricular arrhythmias</kwd></kwd-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Гордеева М.В., Митрофанова Л.Б., Пахомов А.В. и др. Внезапная сердечная смерть молодых людей. // Вестник аритмологии. - 2011. - № 68. - С. 34-44.</mixed-citation><mixed-citation xml:lang="en">Гордеева М.В., Митрофанова Л.Б., Пахомов А.В. и др. Внезапная сердечная смерть молодых людей. // Вестник аритмологии. - 2011. - № 68. - С. 34-44.</mixed-citation></citation-alternatives></ref><ref id="cit2"><label>2</label><citation-alternatives><mixed-citation xml:lang="ru">Земцовский Э.В., Малев Э.Г. Малые аномалии сердца и диспластические фенотипы.- СПб. : Издательство «ИВЭСЭП», 2012,160 с.</mixed-citation><mixed-citation xml:lang="en">Земцовский Э.В., Малев Э.Г. Малые аномалии сердца и диспластические фенотипы.- СПб. : Издательство «ИВЭСЭП», 2012,160 с.</mixed-citation></citation-alternatives></ref><ref id="cit3"><label>3</label><citation-alternatives><mixed-citation xml:lang="ru">Земцовский Э.В., Малев Э.Г., Лунева Е.Б. Наследственные нарушения соединительной ткани и внезапная смерть. // Вестник аритмологии. - 2011. - №63. - С.61-65. ВЕСТНИК АРИТМОЛОГИИ, № 69, 2012</mixed-citation><mixed-citation xml:lang="en">Земцовский Э.В., Малев Э.Г., Лунева Е.Б. Наследственные нарушения соединительной ткани и внезапная смерть. // Вестник аритмологии. - 2011. - №63. - С.61-65. ВЕСТНИК АРИТМОЛОГИИ, № 69, 2012</mixed-citation></citation-alternatives></ref><ref id="cit4"><label>4</label><citation-alternatives><mixed-citation xml:lang="ru">Митрофанова Л.Б., Аминева Х.К. Пособие для врачей под редакцией проф. Г.Б.Ковальского «Макроскопический и органометрический анализ сердца в патологии». Городское патологоанатомическое бюро. Санкт-Петербург 1998, с 58.</mixed-citation><mixed-citation xml:lang="en">Митрофанова Л.Б., Аминева Х.К. Пособие для врачей под редакцией проф. Г.Б.Ковальского «Макроскопический и органометрический анализ сердца в патологии». Городское патологоанатомическое бюро. Санкт-Петербург 1998, с 58.</mixed-citation></citation-alternatives></ref><ref id="cit5"><label>5</label><citation-alternatives><mixed-citation xml:lang="ru">Митрофанова Л.Б., Бещук О.В., Татарский Р.Б., Лебедев Д.С. Аритмогенная кардиомиопатия правого желудочка и вирусная инфекция: возможные сочетания и роль в генезе желудочковых тахиаритмий. // Вестник аритмологии. - 2010. - № 58. - С. 15-20.</mixed-citation><mixed-citation xml:lang="en">Митрофанова Л.Б., Бещук О.В., Татарский Р.Б., Лебедев Д.С. Аритмогенная кардиомиопатия правого желудочка и вирусная инфекция: возможные сочетания и роль в генезе желудочковых тахиаритмий. // Вестник аритмологии. - 2010. - № 58. - С. 15-20.</mixed-citation></citation-alternatives></ref><ref id="cit6"><label>6</label><citation-alternatives><mixed-citation xml:lang="ru">Митрофанова Л.Б., Бещук О.В., Наумова Е.Ю. Диагностика аритмогенной дисплазии правого желудочка по эндомиокардиальной биопсии и роль вирусов в патогенезе заболевания. // Архив патологии. - 2011.- №5. - С. 27-30.</mixed-citation><mixed-citation xml:lang="en">Митрофанова Л.Б., Бещук О.В., Наумова Е.Ю. Диагностика аритмогенной дисплазии правого желудочка по эндомиокардиальной биопсии и роль вирусов в патогенезе заболевания. // Архив патологии. - 2011.- №5. - С. 27-30.</mixed-citation></citation-alternatives></ref><ref id="cit7"><label>7</label><citation-alternatives><mixed-citation xml:lang="ru">ACC/AHA 2006 guidelines for the management of patients with valvular heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines. // Journal of the American College of Cardiology.- 2006.- 48. (3) - P:1-148.</mixed-citation><mixed-citation xml:lang="en">ACC/AHA 2006 guidelines for the management of patients with valvular heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines. // Journal of the American College of Cardiology.- 2006.- 48. (3) - P:1-148.</mixed-citation></citation-alternatives></ref><ref id="cit8"><label>8</label><citation-alternatives><mixed-citation xml:lang="ru">ACC/AHA/ESC 2006 guidelines for management of patients with ventricular arrhythmias and the prevention of sudden cardiac death: a report of the American College of Cardiology/American Heart Association Task Force and the European Society of Cardiology Committee for Practice Guidelines (Writing Committee to Develop Guidelines for Management of Patients With Ventricular Arrhythmias and the Prevention of Sudden Cardiac Death). // JACC.-2006 Sep 5;48(5)- P.247-346.</mixed-citation><mixed-citation xml:lang="en">ACC/AHA/ESC 2006 guidelines for management of patients with ventricular arrhythmias and the prevention of sudden cardiac death: a report of the American College of Cardiology/American Heart Association Task Force and the European Society of Cardiology Committee for Practice Guidelines (Writing Committee to Develop Guidelines for Management of Patients With Ventricular Arrhythmias and the Prevention of Sudden Cardiac Death). // JACC.-2006 Sep 5;48(5)- P.247-346.</mixed-citation></citation-alternatives></ref><ref id="cit9"><label>9</label><citation-alternatives><mixed-citation xml:lang="ru">Asimaki A., Saffitz J. The Role of Endomyocardial Biopsy in ARVC: Looking Beyond Histology in Search of New Diagnostic Markers // Cardiovascular Electrophysiology. - 2011. - Vol. 22, No. 1 - P.111-117.</mixed-citation><mixed-citation xml:lang="en">Asimaki A., Saffitz J. The Role of Endomyocardial Biopsy in ARVC: Looking Beyond Histology in Search of New Diagnostic Markers // Cardiovascular Electrophysiology. - 2011. - Vol. 22, No. 1 - P.111-117.</mixed-citation></citation-alternatives></ref><ref id="cit10"><label>10</label><citation-alternatives><mixed-citation xml:lang="ru">Azaouagh A., Churzidse S., Konorza T., et al. Arrhythmogenic right ventricular cardiomyopathy/dysplasia: a review and update. // Clin Res Cardiol. -2011. - Vol.100.-P.383-394.</mixed-citation><mixed-citation xml:lang="en">Azaouagh A., Churzidse S., Konorza T., et al. Arrhythmogenic right ventricular cardiomyopathy/dysplasia: a review and update. // Clin Res Cardiol. -2011. - Vol.100.-P.383-394.</mixed-citation></citation-alternatives></ref><ref id="cit11"><label>11</label><citation-alternatives><mixed-citation xml:lang="ru">Basso C., Pilichou K.,Carturan E, et al. Pathobiology of Arrhythmogenic Cardiomyopathy. // Card Electrophysiol Clin 3 -2011- P.193-204.</mixed-citation><mixed-citation xml:lang="en">Basso C., Pilichou K.,Carturan E, et al. Pathobiology of Arrhythmogenic Cardiomyopathy. // Card Electrophysiol Clin 3 -2011- P.193-204.</mixed-citation></citation-alternatives></ref><ref id="cit12"><label>12</label><citation-alternatives><mixed-citation xml:lang="ru">Basso C., Ronco F., Marcus F. et al. Quantitative assessment of endomyocardial biopsy in arrhythmogenic right ventricular: an in vitro validation of diagnostic criteria. // Eur. Heart J. - 2008. - Vol. 29. - P. 2760-2771.</mixed-citation><mixed-citation xml:lang="en">Basso C., Ronco F., Marcus F. et al. Quantitative assessment of endomyocardial biopsy in arrhythmogenic right ventricular: an in vitro validation of diagnostic criteria. // Eur. Heart J. - 2008. - Vol. 29. - P. 2760-2771.</mixed-citation></citation-alternatives></ref><ref id="cit13"><label>13</label><citation-alternatives><mixed-citation xml:lang="ru">Basso C., Corrado D., Marcus F. et al. Arrhythmogenic right ventricular cardiomyopathy // Lancet. - 2009. - Vol. 373. - P. 1289-1300.</mixed-citation><mixed-citation xml:lang="en">Basso C., Corrado D., Marcus F. et al. Arrhythmogenic right ventricular cardiomyopathy // Lancet. - 2009. - Vol. 373. - P. 1289-1300.</mixed-citation></citation-alternatives></ref><ref id="cit14"><label>14</label><citation-alternatives><mixed-citation xml:lang="ru">Basso C., Thiene G. Adipositas cordis, fatty infiltration of the right ventricle, and arrhythmogenic right ventricular cardiomyopathy. Just a matter of fat? // Cardiovasc. Pathol. - 2005. - Vol. 14. - P. 37-41.</mixed-citation><mixed-citation xml:lang="en">Basso C., Thiene G. Adipositas cordis, fatty infiltration of the right ventricle, and arrhythmogenic right ventricular cardiomyopathy. Just a matter of fat? // Cardiovasc. Pathol. - 2005. - Vol. 14. - P. 37-41.</mixed-citation></citation-alternatives></ref><ref id="cit15"><label>15</label><citation-alternatives><mixed-citation xml:lang="ru">Billman G.E, Lappi M.D. Effects of cocaine on cardiac vagal tone before and during coronary artery occlusion: cocaine exacerbates the autonomic response to myocardial ischemia. //J Cardiovasc. Pharmacol.-1993.- Vol.22. - P.869-876.</mixed-citation><mixed-citation xml:lang="en">Billman G.E, Lappi M.D. Effects of cocaine on cardiac vagal tone before and during coronary artery occlusion: cocaine exacerbates the autonomic response to myocardial ischemia. //J Cardiovasc. Pharmacol.-1993.- Vol.22. - P.869-876.</mixed-citation></citation-alternatives></ref><ref id="cit16"><label>16</label><citation-alternatives><mixed-citation xml:lang="ru">Bowles N.E., Ni J., Marcus F. et al. The detection of cardiotropic viruses in the myocardium of patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy. // JACC. - 2002. - Vol. 39. - P. 892-895.</mixed-citation><mixed-citation xml:lang="en">Bowles N.E., Ni J., Marcus F. et al. The detection of cardiotropic viruses in the myocardium of patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy. // JACC. - 2002. - Vol. 39. - P. 892-895.</mixed-citation></citation-alternatives></ref><ref id="cit17"><label>17</label><citation-alternatives><mixed-citation xml:lang="ru">Corrado D., Basso C., Nava A. et al. Sudden death in young people with apparently isolated mitral valve prolapse. // G Ital Cardiol. -1998.- May28(5) -P.600-602.</mixed-citation><mixed-citation xml:lang="en">Corrado D., Basso C., Nava A. et al. Sudden death in young people with apparently isolated mitral valve prolapse. // G Ital Cardiol. -1998.- May28(5) -P.600-602.</mixed-citation></citation-alternatives></ref><ref id="cit18"><label>18</label><citation-alternatives><mixed-citation xml:lang="ru">Corrado D.,Basso C., Thiene G. et al. Spectrum of clinicopathologic manifestations of arrhythmogenic right ventricular cardiomyopathy/dysplasia: a multicenter study // JACC. - 1997. - Vol. 30. - P. 1512-1520.</mixed-citation><mixed-citation xml:lang="en">Corrado D.,Basso C., Thiene G. et al. Spectrum of clinicopathologic manifestations of arrhythmogenic right ventricular cardiomyopathy/dysplasia: a multicenter study // JACC. - 1997. - Vol. 30. - P. 1512-1520.</mixed-citation></citation-alternatives></ref><ref id="cit19"><label>19</label><citation-alternatives><mixed-citation xml:lang="ru">Corrado D., Thiene G., Nava A. et al. Exercize-related sudden death in the young. (abstract). // Eur. Heart J. - 1993. - Vol. 86. - P. 368A.</mixed-citation><mixed-citation xml:lang="en">Corrado D., Thiene G., Nava A. et al. Exercize-related sudden death in the young. (abstract). // Eur. Heart J. - 1993. - Vol. 86. - P. 368A.</mixed-citation></citation-alternatives></ref><ref id="cit20"><label>20</label><citation-alternatives><mixed-citation xml:lang="ru">Cox M.G.P.J., van der Smagt J.J., Noorman M. et al. Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy Diagnostic Task Force Criteria. Impact of New Task Force Criteria. // Circulation: Arrhythmia and Electrophysiology. - 2010. - Vol. 3. - P. 126-133.</mixed-citation><mixed-citation xml:lang="en">Cox M.G.P.J., van der Smagt J.J., Noorman M. et al. Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy Diagnostic Task Force Criteria. Impact of New Task Force Criteria. // Circulation: Arrhythmia and Electrophysiology. - 2010. - Vol. 3. - P. 126-133.</mixed-citation></citation-alternatives></ref><ref id="cit21"><label>21</label><citation-alternatives><mixed-citation xml:lang="ru">D’amati G., Di Gioia C., Giordano C. et al. Myocyte transdifferentiation: a possible pathogenetic mechanism for arrhythmogenic right ventricular cardiomyopathy. // Arch. Pathol. Lab. Med. - 2000. - Vol. 124. - P. 287-290.</mixed-citation><mixed-citation xml:lang="en">D’amati G., Di Gioia C., Giordano C. et al. Myocyte transdifferentiation: a possible pathogenetic mechanism for arrhythmogenic right ventricular cardiomyopathy. // Arch. Pathol. Lab. Med. - 2000. - Vol. 124. - P. 287-290.</mixed-citation></citation-alternatives></ref><ref id="cit22"><label>22</label><citation-alternatives><mixed-citation xml:lang="ru">Elliott P., Andersson B., Arbustini E. et al. Classification of the cardiomyopathies: a position statement from the European society of cardiology working group on myocardial and pericardial diseases. // Eur. Heart J. - 2008. - Vol. 29 (2). - P. 270-276.</mixed-citation><mixed-citation xml:lang="en">Elliott P., Andersson B., Arbustini E. et al. Classification of the cardiomyopathies: a position statement from the European society of cardiology working group on myocardial and pericardial diseases. // Eur. Heart J. - 2008. - Vol. 29 (2). - P. 270-276.</mixed-citation></citation-alternatives></ref><ref id="cit23"><label>23</label><citation-alternatives><mixed-citation xml:lang="ru">Frias P. Hypertrophic Cardiomyopathy and Arrhythmogenic Right Ventricular Dysplasia in Young Patients. // Elsevier. - 2005- P.25-31.</mixed-citation><mixed-citation xml:lang="en">Frias P. Hypertrophic Cardiomyopathy and Arrhythmogenic Right Ventricular Dysplasia in Young Patients. // Elsevier. - 2005- P.25-31.</mixed-citation></citation-alternatives></ref><ref id="cit24"><label>24</label><citation-alternatives><mixed-citation xml:lang="ru">Geoffroy Lorin de la Grandmaison. Is there progress in the autopsy diagnosis of sudden unexpected death in adults? // Forensic Science International 156 (2006)- P. 138-144.</mixed-citation><mixed-citation xml:lang="en">Geoffroy Lorin de la Grandmaison. Is there progress in the autopsy diagnosis of sudden unexpected death in adults? // Forensic Science International 156 (2006)- P. 138-144.</mixed-citation></citation-alternatives></ref><ref id="cit25"><label>25</label><citation-alternatives><mixed-citation xml:lang="ru">Kapplinger J., BA, Landstrom A., Salisbury B. et al., Distinguishing Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia-Associated Mutations From Background Genetic Noise. // JACC.- Vol. 57, No. 23- 2011 June 7. -P.2317-2327.</mixed-citation><mixed-citation xml:lang="en">Kapplinger J., BA, Landstrom A., Salisbury B. et al., Distinguishing Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia-Associated Mutations From Background Genetic Noise. // JACC.- Vol. 57, No. 23- 2011 June 7. -P.2317-2327.</mixed-citation></citation-alternatives></ref><ref id="cit26"><label>26</label><citation-alternatives><mixed-citation xml:lang="ru">Karatolios K., Pankuweit S., Kisselbach C., Maisch B. Inflammatory cardiomyopathy. // Hellenic J Cardiol. -2006. - Vol.47. - P.54-65.</mixed-citation><mixed-citation xml:lang="en">Karatolios K., Pankuweit S., Kisselbach C., Maisch B. Inflammatory cardiomyopathy. // Hellenic J Cardiol. -2006. - Vol.47. - P.54-65.</mixed-citation></citation-alternatives></ref><ref id="cit27"><label>27</label><citation-alternatives><mixed-citation xml:lang="ru">Lombardi R., Marian A., Molecular Genetics and Pathogenesis of Arrhythmogenic Right Ventricular Cardiomyopathy: A Disease of Cardiac Stem Cells. // Pediatr Cardiol. - 2011- Vol.32. - P.360-365.</mixed-citation><mixed-citation xml:lang="en">Lombardi R., Marian A., Molecular Genetics and Pathogenesis of Arrhythmogenic Right Ventricular Cardiomyopathy: A Disease of Cardiac Stem Cells. // Pediatr Cardiol. - 2011- Vol.32. - P.360-365.</mixed-citation></citation-alternatives></ref><ref id="cit28"><label>28</label><citation-alternatives><mixed-citation xml:lang="ru">Marcus F.I., McKenna W.J., Sherrill D. et al. Diagnosis of Arrhythmogenic Right Ventricular Cardiomyopathy/ Dysplasia. Proposed Modification of the Task Force Criteria. // Circulation. - 2010. - Vol. 121. - P. 1533-1541.</mixed-citation><mixed-citation xml:lang="en">Marcus F.I., McKenna W.J., Sherrill D. et al. Diagnosis of Arrhythmogenic Right Ventricular Cardiomyopathy/ Dysplasia. Proposed Modification of the Task Force Criteria. // Circulation. - 2010. - Vol. 121. - P. 1533-1541.</mixed-citation></citation-alternatives></ref><ref id="cit29"><label>29</label><citation-alternatives><mixed-citation xml:lang="ru">McKenna W.J., Thiene G., Nava A. et al. Diagnosis of arrhythmogenic right ventricular dysplasia/cardiomyopathy: Task Force of the Working Group Myocardial and Pericardial Disease of the European Society of Cardiology and of the Scientific Council on Cardiomyopathies of the International Society and Federation of Cardiology. // Br Heart J.- 1994. - Vol. 71. - P. 215-218.</mixed-citation><mixed-citation xml:lang="en">McKenna W.J., Thiene G., Nava A. et al. Diagnosis of arrhythmogenic right ventricular dysplasia/cardiomyopathy: Task Force of the Working Group Myocardial and Pericardial Disease of the European Society of Cardiology and of the Scientific Council on Cardiomyopathies of the International Society and Federation of Cardiology. // Br Heart J.- 1994. - Vol. 71. - P. 215-218.</mixed-citation></citation-alternatives></ref><ref id="cit30"><label>30</label><citation-alternatives><mixed-citation xml:lang="ru">Nishikawa T., Ishiyama S., Nagata M. et al. Ptogrammed cell death in the myocardium of arrhythmogenic right ventricular cardiomyopathy in children and adults. // Cardiovasc Pathol. - 1999. - Vol.8. - P.185-189.</mixed-citation><mixed-citation xml:lang="en">Nishikawa T., Ishiyama S., Nagata M. et al. Ptogrammed cell death in the myocardium of arrhythmogenic right ventricular cardiomyopathy in children and adults. // Cardiovasc Pathol. - 1999. - Vol.8. - P.185-189.</mixed-citation></citation-alternatives></ref><ref id="cit31"><label>31</label><citation-alternatives><mixed-citation xml:lang="ru">Peng S.K, French W.J, Pelikan P.C. Direct cocaine cardiotoxicity demonstrated by endomyocardial biopsy. //Arch Pathol Lab Med -1989.- Vol.113. - P.842-845.</mixed-citation><mixed-citation xml:lang="en">Peng S.K, French W.J, Pelikan P.C. Direct cocaine cardiotoxicity demonstrated by endomyocardial biopsy. //Arch Pathol Lab Med -1989.- Vol.113. - P.842-845.</mixed-citation></citation-alternatives></ref><ref id="cit32"><label>32</label><citation-alternatives><mixed-citation xml:lang="ru">Peters S., Trummel M., Meyners W. Prevalence of right ventricular dysplasia-cardiomyopathy in a non-referral cardiomyopathy and sudden death in young people. // N. Engl. J. Med. - 1988. - Vol. 318. - P. 129-133</mixed-citation><mixed-citation xml:lang="en">Peters S., Trummel M., Meyners W. Prevalence of right ventricular dysplasia-cardiomyopathy in a non-referral cardiomyopathy and sudden death in young people. // N. Engl. J. Med. - 1988. - Vol. 318. - P. 129-133</mixed-citation></citation-alternatives></ref><ref id="cit33"><label>33</label><citation-alternatives><mixed-citation xml:lang="ru">Valente M., Calabrese F., Thiene G. et al. In vivo evidence of apoptosis in arrhythmogenic right ventricular cardiomyopathy. // Am. J. Pathol. - 1998. - Vol. 152. - P. 479484.</mixed-citation><mixed-citation xml:lang="en">Valente M., Calabrese F., Thiene G. et al. In vivo evidence of apoptosis in arrhythmogenic right ventricular cardiomyopathy. // Am. J. Pathol. - 1998. - Vol. 152. - P. 479484.</mixed-citation></citation-alternatives></ref><ref id="cit34"><label>34</label><citation-alternatives><mixed-citation xml:lang="ru">Virmani R., Burke A.R. and Farb A. Pathologic experience in USA. In Nava A., Rossi L., editors: Arrhythmogenic right ventricular cardiomyopathy/dysplasia. // Elsevier, Amsterdam, - 1997. - P. 87-93.</mixed-citation><mixed-citation xml:lang="en">Virmani R., Burke A.R. and Farb A. Pathologic experience in USA. In Nava A., Rossi L., editors: Arrhythmogenic right ventricular cardiomyopathy/dysplasia. // Elsevier, Amsterdam, - 1997. - P. 87-93.</mixed-citation></citation-alternatives></ref><ref id="cit35"><label>35</label><citation-alternatives><mixed-citation xml:lang="ru">Vreede Swagemakers J.J.M., Gorgels A.P.M., Dubois-Arbouw W.I. et al. Out-of-hospital cardiac arrest in the 1990s: a population-based study in the Maastricht area on incidence, characteristics and survival. // J. Am. Coll. Cardiol. - 1997. - Vol.30. - P. 1500-1505.</mixed-citation><mixed-citation xml:lang="en">Vreede Swagemakers J.J.M., Gorgels A.P.M., Dubois-Arbouw W.I. et al. Out-of-hospital cardiac arrest in the 1990s: a population-based study in the Maastricht area on incidence, characteristics and survival. // J. Am. Coll. Cardiol. - 1997. - Vol.30. - P. 1500-1505.</mixed-citation></citation-alternatives></ref><ref id="cit36"><label>36</label><citation-alternatives><mixed-citation xml:lang="ru">Warren Smith, FRACP, Members of the CSANZ Cardiovascular Genetics Working Group. Guidelines for the Diagnosis and Management of Arrhythmogenic Right Ventricular Cardiomyopathy. // Heart, Lung and Circulation. - 2011. - Vol.20 -P.757-760. hospital.// Int. J. Cardiol. - 2004. - Vol. 97. - P. 499-501.</mixed-citation><mixed-citation xml:lang="en">Warren Smith, FRACP, Members of the CSANZ Cardiovascular Genetics Working Group. Guidelines for the Diagnosis and Management of Arrhythmogenic Right Ventricular Cardiomyopathy. // Heart, Lung and Circulation. - 2011. - Vol.20 -P.757-760. hospital.// Int. J. Cardiol. - 2004. - Vol. 97. - P. 499-501.</mixed-citation></citation-alternatives></ref><ref id="cit37"><label>37</label><citation-alternatives><mixed-citation xml:lang="ru">Puranik R., Chow C.R., Duflou J.A. et al. Sudden death in the young. // Heart Rhythm. -2005. - Vol. 2. - N 12. - P. 1277-1282.</mixed-citation><mixed-citation xml:lang="en">Puranik R., Chow C.R., Duflou J.A. et al. Sudden death in the young. // Heart Rhythm. -2005. - Vol. 2. - N 12. - P. 1277-1282.</mixed-citation></citation-alternatives></ref><ref id="cit38"><label>38</label><citation-alternatives><mixed-citation xml:lang="ru">Saffitz J.E., Dependence of electrical coupling on mechanical coupling in cardiac myocytes: insights gained from cardiomyopathies caused by defects in cell-cell connections. // Ann.N. Y. Acad. Sci. - 2005. - Vol. 1047. - P. 336 -344.</mixed-citation><mixed-citation xml:lang="en">Saffitz J.E., Dependence of electrical coupling on mechanical coupling in cardiac myocytes: insights gained from cardiomyopathies caused by defects in cell-cell connections. // Ann.N. Y. Acad. Sci. - 2005. - Vol. 1047. - P. 336 -344.</mixed-citation></citation-alternatives></ref><ref id="cit39"><label>39</label><citation-alternatives><mixed-citation xml:lang="ru">Sen-Chowdhry S., Syrris P., Prasad S.K. et al. Left-dominant arrhythmogenic cardiomyopathy: an under-recognized clinical entity. // JACC. - 2008. - Vol. 52. - P. 21752187.</mixed-citation><mixed-citation xml:lang="en">Sen-Chowdhry S., Syrris P., Prasad S.K. et al. Left-dominant arrhythmogenic cardiomyopathy: an under-recognized clinical entity. // JACC. - 2008. - Vol. 52. - P. 21752187.</mixed-citation></citation-alternatives></ref><ref id="cit40"><label>40</label><citation-alternatives><mixed-citation xml:lang="ru">Sen-Chowdhry S.,Syrris P, Quarta G., McKenna W., Clinical Impact of Genetics in Arrhythmogenic Cardiomyopathy // Card. Electrophysiol. Clin. 3. -2011.- p.205-215.</mixed-citation><mixed-citation xml:lang="en">Sen-Chowdhry S.,Syrris P, Quarta G., McKenna W., Clinical Impact of Genetics in Arrhythmogenic Cardiomyopathy // Card. Electrophysiol. Clin. 3. -2011.- p.205-215.</mixed-citation></citation-alternatives></ref><ref id="cit41"><label>41</label><citation-alternatives><mixed-citation xml:lang="ru">Tansey D.K., Aly Z., Sheppard M.N. Fat in the right ventricle of the normal heart. // Histopathology. - 2005. -Vol. 46. - P.98-104.</mixed-citation><mixed-citation xml:lang="en">Tansey D.K., Aly Z., Sheppard M.N. Fat in the right ventricle of the normal heart. // Histopathology. - 2005. -Vol. 46. - P.98-104.</mixed-citation></citation-alternatives></ref></ref-list><fn-group><fn fn-type="conflict"><p>The authors declare that there are no conflicts of interest present.</p></fn></fn-group></back></article>
