References

vestar

Вестник аритмологии

Journal of Arrhythmology

1561-86412658-7327

НАО «Инкарт»

vestar-744

Research Article

ОБЗОРЫ

REVIEWS

АРИТМОГЕННАЯ КАРДИОМИОПАТИЯ/ДИСПЛАЗИЯ ПРАВОГО ЖЕЛУДОЧКА: КЛИНИЧЕСКИЕ И МОЛЕКУЛЯРНО-ГЕНЕТИЧЕСКИЕ ОСОБЕННОСТИ

ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY/DYSPLASIA: CLINICAL AND MOLECULAR GENETIC PECULIAR FEATURES

Федяков

М. А.

Fedyakov

M. A.

noemail@neicon.ru

Велеславова

О. Е.

Veleslavova

O. E.

noemail@neicon.ru

Глотов

О. С.

Glotov

O. S.

noemail@neicon.ru

Апалько

С. В.

Apalko

S. V.

noemail@neicon.ru

Сарана

А. М.

Sarana

A. M.

noemail@neicon.ru

Щербак

С. Г.

Shcherbak

S. G.

noemail@neicon.ru

СПб ГБУЗ «Городская больница № 40»Russian FederationСеверо-западный центр диагностики и лечения аритмий СПбГУRussian FederationСПб ГБУЗ «Городская больница № 40»; Институт трансляционной биомедицины СПбГУRussian FederationСПб ГБУЗ «Городская больница № 40»; СПбГУRussian Federation

2015

23092020

0813341

2020

Федяков М.А., Велеславова О.Е., Глотов О.С., Апалько С.В., Сарана А.М., Щербак С.Г.

Fedyakov M.A., Veleslavova O.E., Glotov O.S., Apalko S.V., Sarana A.M., Shcherbak S.G.

Данная работа распространяется под лицензией Creative Commons Attribution 4.0.

This work is licensed under a Creative Commons Attribution 4.0 License.

https://vestar.elpub.ru/jour/article/view/744

Рассматриваются вопросы этиологии, патогенеза, диагностики и лечения аритмогенной кардиомиопатии/дисплазии правого желудочка, характер ее клинического течения, необходимость профилактики внезапной сердечной смерти.

The problems of etiology, pathogeny, diagnosis, and treatment of arrhythmogenic right ventricular cardiomyopathy/ dysplasia are considered, as well as its clinical course and a need for prevention of sudden cardiac death.

аритмогенная кардиомиопатия/дисплазия правого желудочкавнезапная сердечная смертьфиброзно-жировое замещениежелудочковые тахикардиисеквенирование нового поколенияинтерпретация данных секвенирования

arrhythmogenic right ventricular cardiomyopathy/dysplasiasudden cardiac deathfibro-fatty replacementventricular tachycardianext generation sequencingsequencing data interpretation

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The authors declare that there are no conflicts of interest present.