vestarВестник аритмологииJournal of Arrhythmology1561-86412658-7327НАО «Инкарт»vestar-9Research ArticleОБЗОРЫREVIEWSНЕКОМПАКТНЫЙ МИОКАРД - ЛЕЧЕНИЕ, ПРОГНОЗ, МЕРЫ ПО ПРЕДУПРЕЖДЕНИЮ ВНЕЗАПНОЙ СЕРДЕЧНОЙ СМЕРТИ НА ОСНОВАНИИ СОВРЕМЕННЫХ ИНСТРУМЕНТАЛЬНЫХ КРИТЕРИЕВNON-COMPACTION CARDIOMYOPATHY: MANAGEMENT, OUTCOMES, PREVENTION OF SUDDEN CARDIAC DEATH BASED ON UP-TO-DATE INSTRUMENTAL CRITERIAПроничеваИ. В.PronichevaI. V.noemail@neicon.ruМасловаИ. И.MaslovaI. I.noemail@neicon.ruНЦ ССХ им. А.Н. Бакулева МЗРФRussian Federation2016170420190833843Copyright © Проничева И.В., Маслова И.И., 20192019Проничева И.В., Маслова И.И.Pronicheva I.V., Maslova I.I.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://vestar.elpub.ru/jour/article/view/9

Рассматриваются критерии диагностики редкой генетически гетерогенной кардиомиопатии - некомпактного («губчатого») миокарда, обсуждаются методы его лечения, направленные на профилактику жизнеугрожающих желудочковых аритмий и тромбоэмболических осложнений, коррекцию сердечной недостаточности, профилактику внезапной сердечной смерти.

The diagnostic criteria are considered of a rare genetically heterogeneous cardiomyopathy: non-compaction cardiomyopathy (“spongy” myocardium); management strategies are discussed addressing prevention of life-threatening ventricular arrhythmias and thromboembolic events, as well as prevention of sudden cardiac death.

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The authors declare that there are no conflicts of interest present.