Clinical case of neonatal lupus with cartilaginous metaplasia, fibrosis and calcification of the atrioventricular node zone
https://doi.org/10.35336/VA-2023-2-10
EDN: VZVVWP
Abstract
Neonatal lupus is a rare disease associated with the circulation in the mother’s blood of one or more autoantibodies to soluble intracellular ribonucleoproteins Ro/SS-A and La/SS-B. This disease is extremely often manifested by congenital heart block, which can progress even after the birth of a child. We have described a case of fibrosis, calcification and cartilaginous metaplasia of the atrioventricular node zone, which caused complete atrioventricular block in a child who died from neonatal lupus.
About the Authors
D. A. Davydov
Pavlov First Saint Petersburg State Medical University of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
6-8 Lev Tolstoy str
I. A. Makarov
Almazov National Medical Research Center” of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
A. A. Morozov
Almazov National Medical Research Center” of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
T. A. Makarova
Almazov National Medical Research Center” of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
L. B. Mitrofanova
Almazov National Medical Research Center” of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
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Review
For citations:
Davydov D.A., Makarov I.A., Morozov A.A., Makarova T.A., Mitrofanova L.B. Clinical case of neonatal lupus with cartilaginous metaplasia, fibrosis and calcification of the atrioventricular node zone. Journal of Arrhythmology. 2023;30(2):е1-е5. https://doi.org/10.35336/VA-2023-2-10. EDN: VZVVWP
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