Clinical characteristics of the “hot phase” of arrhythmogenic cardiomyopathy in a pediatric patient
O. A. Kofeynikova,
D. Yu. Alekseeva,
S. G. Fetisova,
E. V. Yakovleva,
O. L. Peregudina,
T. L. Vershinina,
A. A. Kostareva,
E. S. Vasichkina https://doi.org/10.35336/VA-2023-2-11
EDN: WJDXWN
Abstract
This article describes a rare clinical manifestation of arrhythmogenic cardiomyopathy in a 13-year-old boy - the “hot phase”, characterized by severe chest pain and a significant increase on a level of troponin I. The clinical case demonstrates the difficulties of the differential diagnosis of this disease and an importance of an integrated approach to examination of the patient, including cardiac magnetic resonance imaging and genetic testing.
Keywords
arrhythmogenic cardiomyopathy,
“hot phase”,
myocarditis,
children,
sudden cardiac death,
magnetic resonance imaging,
troponin I
Supporting agencies: the study was supported by the Ministry of Science and Higher Education of the Russian Federation (Agreement No. 075-15-2022-301 dated April 20, 2022).
About the Authors
O. A. Kofeynikova
Almazov National Medical Research Center
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
D. Yu. Alekseeva
Almazov National Medical Research Center
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
S. G. Fetisova
Almazov National Medical Research Center
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
E. V. Yakovleva
Almazov National Medical Research Center
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
O. L. Peregudina
Almazov National Medical Research Center
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
T. L. Vershinina
Almazov National Medical Research Center
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
A. A. Kostareva
Almazov National Medical Research Center
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
E. S. Vasichkina
Almazov National Medical Research Center
Russian Federation
Russian Federation
Saint-Petersburg, 2 Akkuratova str.
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Review
For citations:
Kofeynikova O.A., Alekseeva D.Yu., Fetisova S.G., Yakovleva E.V., Peregudina O.L., Vershinina T.L., Kostareva A.A., Vasichkina E.S. Clinical characteristics of the “hot phase” of arrhythmogenic cardiomyopathy in a pediatric patient. Journal of Arrhythmology. 2023;30(2):е6-е11. https://doi.org/10.35336/VA-2023-2-11. EDN: WJDXWN
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